This condition is a rare congenital malformation, also known as ulnar club hand, less common than radial club hand. It is usually unilateral, with the right side being more common, and male patients are more than female patients. The children have the thumb and index finger, with good activity function, but the ulnar side is absent. The affected forearm is thin, short, and inclined towards the ulnar side, with the radial head dislocation, limited rotation function of the forearm, but the wrist and elbow joints function well. The patients may also have the absence of wrist bones, commonly the navicular bone, hamate bone, trapezium bone, and capitate bone. Sometimes the fourth and fifth metacarpal bones may also be absent. The radius bows outward, becoming more obvious with the growth of the child. About 20% of the children have syndactyly. Other associated deformities include the absence of the fibula, clubfoot, and spina bifida, etc.