Nephroureteral cyst is a cystic dilatation at the distal end of the ureter. The failure of absorption and regression of the membrane between the ureter and the urogenital sinus during embryonic development can lead to varying degrees of narrowing at the ureteral orifice. It can also be caused by factors such as weak fibrous structures at the distal end of the ureter or an excessively long and tortuous course in the interstitial segment, which can form a cystic dilatation protruding into the bladder after being impacted by urinary flow. In early cases, there may be no clinical symptoms, and it is often discovered during the diagnosis of renal malformation. Symptoms are mainly due to urinary tract obstruction, leading to recurrent urinary tract infections. Due to the small opening of the cyst, persistent obstruction at the ureteral orifice can cause hydronephrosis and renal atrophy, loss of renal function, difficulty in urination or interruption of urinary flow due to cystic obstruction of the bladder neck, and recurrent urinary tract infections. Sometimes, a girl's cyst can prolapse through the bladder neck and urethra to the outside of the urethral orifice, which can generally be复位自行复位. However, it can also become an incarcerated purple mass. The principle of treatment is to relieve obstruction, prevent reflux, and manage complications. If the upper half of the renal function on the affected side is poor, a heminephrectomy can be performed. About 20-25% of cases still have symptoms after surgery, and the cyst should be treated again at this time. If the renal function of the affected kidney is good, a ureteral cystectomy and anti-reflux ureteral bladder reimplantation can be performed.